Klinische Klassifikation der pulmonalen Hypertonie und initiale Diagnostik: Empfehlungen der Kölner Konsensus Konferenz 2016

G. Kovacs; D. Dumitrescu; A. Barner; S. Greiner; E. Grünig; A. Hager; T. Köhler; R. Kozlik-Feldmann; I. Kruck; A. Lammers; D. Mereles; A. Meyer; F. J. Meyer; S. Pabst; H.-J. Seyfarth; C. Sinning; S. Sorichter; G. Stähler; H. Wilkens; M. Held

doi:10.1055/s-0042-114523

DMW - Deutsche Medizinische Wochenschrift, Inhaltsverzeichnis

Dtsch Med Wochenschr 2016; 141(S 01): S10-S18
DOI: 10.1055/s-0042-114523

Pulmonale Hypertonie: Empfehlungen der Kölner Konsensus-Konferenz 2016

Klinische Klassifikation der pulmonalen Hypertonie und initiale Diagnostik: Empfehlungen der Kölner Konsensus Konferenz 2016

Clinical classification and initial diagnosis of pulmonary hypertension: recommendations of the Cologne Consensus Conference 2016

G. Kovacs^*

¹Klinische Abteilung für Lungenkrankheiten, Universitätsklinik für Innere Medizin, Medizinische Universität Graz

²Ludwig Boltzmann Institut für Lungengefäßforschung, Graz

,

D. Dumitrescu^*

³Klinik III für Innere Medizin, Herzzentrum der Universität zu Köln

,

A. Barner

⁴Krankenhaus & Sanatorium Dr. Barner, Braunlage

,

S. Greiner

⁵Abteilung Innere Medizin III, Kardiologie, Angiologie und Pneumologie, Universitätsklinikum Heidelberg

,

E. Grünig

⁶Zentrum für Pulmonale Hypertonie, Thoraxklinik am Universitätsklinikum Heidelberg

,

A. Hager

⁷Klinik für Kinderkardiologie und angeborene Herzfehler, Deutsches Herzzentrum München

,

T. Köhler

⁸Klinik für Pneumologie, Department Innere Medizin, Universitätsklinikum Freiburg

,

R. Kozlik-Feldmann

⁹Klinik und Poliklinik für Kinderkardiologie, Universitäres Herzzentrum Hamburg GmbH, Universitätsklinikum Eppendorf, Hamburg

,

I. Kruck

¹⁰Cardio Centrum Ludwigsburg Bietigheim, Ludwigsburg

,

A. Lammers

¹¹Spezialambulanz Pädiatrische Pulmonale Hypertonie, Pädiatrische Kardiologie, Universitätsklinikum Münster

,

D. Mereles

⁵Abteilung Innere Medizin III, Kardiologie, Angiologie und Pneumologie, Universitätsklinikum Heidelberg

,

A. Meyer

¹²Klinik für Pneumologie, Krankenhaus St. Franziskus, Mönchengladbach

,

F. J. Meyer

¹³Lungenzentrum München, Städtisches Klinikum München GmbH

,

S. Pabst

¹⁴Sektion Pneumologie, Medizinische Klinik und Poliklinik II, Universitätsklinikum Bonn

,

H.-J. Seyfarth

¹⁵Abteilung Pneumologie, Department Innere Medizin, Neurologie und Dermatologie, Universitätsklinik Leipzig

,

C. Sinning

¹⁶Universitäres Herzzentrum Hamburg, Klinik für Allgemeine und Interventionelle Kardiologie, Hamburg

,

S. Sorichter

¹⁷Klinik für Pneumologie und Beatmungsmedizin, St.-Josefskrankenhaus, RkK-Klinikum Freiburg

,

G. Stähler

¹⁸Medizinische Klinik I, Klinik Löwenstein

,

H. Wilkens

¹⁹Klinik für Innere Medizin V, Pneumologie, Universitätsklinikum des Saarlandes, Homburg

,

M. Held

²⁰Zentrum für pulmonale Hypertonie und Lungengefäßerkrankungen, Abteilung Innere Medizin, Missionsärztliche Klinik Würzburg

› Institutsangaben

Abstract

Zusammenfassung

Die 2015 veröffentlichten Europäischen Leitlinien zur Diagnostik und Therapie der pulmonalen Hypertonie (PH) sind nunmehr auch in Deutschland gültig. Die Leitlinien befassen sich eingehend mit der Klassifikation und Diagnostik der PH, und bieten darüber hinaus neue Empfehlungen zur Risikostratifizierung und Verlaufskontrollen bei Patienten mit diagnostizierter PAH. Für die praktische Umsetzung der Europäischen Leitlinien in Deutschland sind jedoch zahlreiche für Deutschland spezifische Gesichtspunkte und bereits wieder neue Daten bedeutsam, die eine ausführliche Kommentierung der Leitlinien und in einigen Punkten eine Aktualisierung notwendig machen. Im Juni 2016 fand in Köln eine Konsensus-Konferenz statt, die von den Arbeitsgruppen PH der Deutschen Gesellschaften für Kardiologie (DGK), Pneumologie (DGP) und Pädiatrische Kardiologie (DGPK) organisiert wurde. Die Konferenz befasste sich mit der Umsetzung der Europäischen Leitlinien im deutschsprachigen Raum. Dazu wurden verschiedene Arbeitsgruppen eingesetzt, von denen sich eine gezielt der Klassifikation und initialen Diagnostik der PH widmete. Die Ergebnisse und Beschlüsse dieser Arbeitsgruppe werden in dem vorliegenden Manuskript detailliert beschrieben.

Abstract

The 2015 European Guidelines on Diagnosis and Treatment of Pulmonary Hypertension are also valid for Germany. The guidelines contain detailed information about the clinical classification and diagnosis of pulmonary hypertension, and furthermore provide novel recommendations for risk stratification and follow-up assessments. However, the practical implementation of the European Guidelines in Germany requires the consideration of several country-specific issues and already existing novel data. This requires a detailed commentary to the guidelines, and in some aspects an update already appears necessary. In June 2016, a Consensus Conference organized by the PH working groups of the German Society of Cardiology (DGK), the German Society of Respiratory Medicine (DGP) and the German Society of Pediatric Cardiology (DGPK) was held in Cologne, Germany. This conference aimed to solve practical and controversial issues surrounding the implementation of the European Guidelines in Germany. To this end, a number of working groups was initiated, one of which was specifically dedicated to the clinical classification and initial diagnosis of PH. This article summarizes the results and recommendations of this working group.

Schlüsselwörter

pulmonale Hypertonie - Diagnostik - Klassifikation - Definition

Keywords

pulmonary hypertension - diagnosis - classification - definition

Volltext

Referenzen

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