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CC BY-NC-ND 4.0 · Thorac Cardiovasc Surg Rep 2022; 11(01): e20-e22
DOI: 10.1055/s-0042-1742781
Case Report: Thoracic

Extrapleural Pneumonectomy for Sarcoma of the Lung in a Pediatric Patient

Michael Schweigert 
1   Department of Surgery, University Hospital Schleswig-Holstein, Luebeck, Germany
,
Ana B. Almeida
1   Department of Surgery, University Hospital Schleswig-Holstein, Luebeck, Germany
,
Jessica Pablik
2   Department of Pathology, University Hospital, Dresden, Germany
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Abstract

Pediatric sarcomas are rare entities. Bone sarcomas and rhabdomyosarcoma are most common, whereas primary sarcoma of the lung is extremely uncommon. Pneumonectomy is only very infrequently performed in the pediatric population. We report on a 16-year-old girl with an undifferentiated high-grade pleomorphic sarcoma of the left lung. There was no comorbidity and no history of previous malignant disease. The huge tumor originated from the left lower lobe and had spread to the left pleura. As part of a multimodal approach, she underwent extrapleural pneumonectomy with en bloc resection of the pleura, lung, pericardium, and diaphragm.

Keywords

pediatric sarcoma - pediatric thoracic surgery - extrapleural pneumonectomy

Note

This study was presented at the 29th European Conference on General Thoracic Surgery, June 20–22, 2021 (Virtual ESTS Meeting).




Publication History

Received: 07 July 2021

Accepted: 18 November 2021

Article published online:
03 March 2022

© 2022. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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