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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2022; 32(01): 145-148
DOI: 10.1055/s-0042-1743115
Case Report

Bony Cyst in a Ground Glass Matrix: A Rare Case Report of Craniofacial Fibrous Dysplasia with Secondary Aneurysmal Bone Cyst

Chandrika Sachar 
1   Department of Radiodiagnosis and Imaging, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
,
Aakanksha Agarwal 
1   Department of Radiodiagnosis and Imaging, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
,
Anjum Syed 
1   Department of Radiodiagnosis and Imaging, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
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Abstract

Fibrous dysplasia has various ways of presentation including syndromic associations and secondary changes within the lesion. We present a case of a 21-year-old female with craniofacial fibrous dysplasia, presenting with proptosis and intermittent blurring of vision due to focal fibrous dysplasia involving the frontal bone with secondary aneurysmal bone formation that was provisionally diagnosed on imaging and confirmed on histopathology. This case demonstrates the typical imaging findings of fibrous dysplasia with seldom encountered secondary aneurysmal bone cyst formation and also discusses about the pathology and management of the craniofacial fibrous dysplasia.

Keywords

craniofacial fibrous dysplasia - secondary aneurysmal bone cyst - tumor

Ethics Approval

Appropriate consent from the patient was obtained. Anonymity of patient has been maintained throughout the case report.


Consent to Participate

Appropriate consent from the patient was obtained.


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All authors give consent for publication of the manuscript in your esteemed journal.


Authors' Contributions

All authors have contributed to the conceptualization, design, acquisition of data, drafting, and review of this article and approved the version to be published.




Publication History

Article published online:
01 May 2022

© 2022. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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  • References

  • 1 Pardo-Maza A, Lassaletta L, Ruiz-Bravo E, Perez-Mora R, Peñarrocha J, Gavilan J. Fibrous dysplasia of the temporal bone secondary to ear surgery: a case report. J Med Case Reports 2015; 9 (01) 129
    CrossrefPubMedSearch in Google Scholar
  • 2 Chong VFH, Khoo JBK, Fan YF. Fibrous dysplasia involving the base of the skull. AJR Am J Roentgenol 2002; 178 (03) 717-720
    CrossrefPubMedSearch in Google Scholar
  • 3 Snieders MN, van Kemenade FJ, van Royen BJ. Monostotic fibrous dysplasia of a lumbar vertebral body with secondary aneurysmal bone cyst formation: a case report. J Med Case Reports 2009; 3: 7227
    CrossrefPubMedSearch in Google Scholar
  • 4 Kushchayeva YS, Kushchayev SV, Glushko TY. et al. Fibrous dysplasia for radiologists: beyond ground glass bone matrix. Insights Imaging 2018; 9 (06) 1035-1056
    CrossrefPubMedSearch in Google Scholar
  • 5 MacDonald-Jankowski D. Fibrous dysplasia: a systematic review. Dentomaxillofac Radiol 2009; 38 (04) 196-215
    CrossrefPubMedSearch in Google Scholar
  • 6 Sachdeva K. Extensive craniofacial fibrous dysplasia: an overview. Clin Rhinol 2017; 10 (01) 17-21
    Search in Google Scholar
  • 7 Nager GT, Holliday MJ. Fibrous dysplasia of the temporal bone. Update with case reports. Ann Otol Rhinol Laryngol 1984; 93 (6 Pt 1): 630-633
    CrossrefPubMedSearch in Google Scholar
  • 8 Diercks RL, Sauter AJ, Mallens WM. Aneurysmal bone cyst in association with fibrous dysplasia. A case report. J Bone Joint Surg Br 1986; 68 (01) 144-146
    CrossrefPubMedSearch in Google Scholar
  • 9 Atalar MH, Salk I, Savas R, Uysal IO, Egilmez H. MR imaging in a large series of patients with craniofacial fibrous dysplasia. Pol J Radiol 2015; 80 (01) 232-240
    PubMedSearch in Google Scholar
  • 10 Collins MT, Kushner H, Reynolds JC. et al. An instrument to measure skeletal burden and predict functional outcome in fibrous dysplasia of bone. J Bone Miner Res 2005; 20 (02) 219-226
    CrossrefPubMedSearch in Google Scholar
  • 11 Javaid MK, Boyce A, Appelman-Dijkstra N. et al. Best practice management guidelines for fibrous dysplasia/McCune-Albright syndrome: a consensus statement from the FD/MAS international consortium. Orphanet J Rare Dis 2019; 14 (01) 1-17
    PubMedSearch in Google Scholar
  • 12 Atasoy C, Ustüner E, Erden I, Akyar S. Frontal sinus mucocele: a rare complication of craniofacial fibrous dysplasia. Clin Imaging 2001; 25 (06) 388-391
    CrossrefPubMedSearch in Google Scholar
  • 13 Ruggieri P, Sim FH, Bond JR, Unni KK. Malignancies in fibrous dysplasia. Cancer 1994; 73 (05) 1411-1424
    CrossrefPubMedSearch in Google Scholar
  • 14 Papadakis CE, Skoulakis CE, Prokopakis EP. et al. Fibrous dysplasia of the temporal bone: report of a case and a review of its characteristics. Ear Nose Throat J 2000; 79 (01) 52-57
    CrossrefPubMedSearch in Google Scholar