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J Am Acad Audiol 2000; 11(06): 300-308
DOI: 10.1055/s-0042-1748058
Case Report

Catastrophic Progressive Hearing Loss in Childhood

Deborah Hayes
Department of Pediatrics, University of Colorado School of Medicine, Denver, Colorado
The Children's Hospital, Audiology Service, Denver, Colorado
,
Susan Dreith
The Children's Hospital, Audiology Service, Denver, Colorado
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Abstract

We present a report on a 5-year-old child with a complex medical and audiologic history who exhibited catastrophic progression in hearing loss. Hearing loss was initially attributed to bacterial meningitis at age 3 months; progression was apparently related to perilymph fistula at age 8 years. Etiologies associated with progressive hearing loss in children as well as signs of progression and monitoring protocols for children at risk for progressive hearing loss are discussed.

Abbreviations: ABR = auditory brainstem response, CMV = cytomegalovirus, JCIH = Joint Committee on Infant Hearing, LVA = large vestibular aqueduct, PPHN = persistent pulmonary hypertension of the newborn, TCH = The Children's Hospital

Key Words

Cytomegalovirus - hearing loss - meningitis


Publication History

Article published online:
08 April 2022

© 2000. American Academy of Audiology. This article is published by Thieme.

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