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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2023; 33(02): 235-239
DOI: 10.1055/s-0042-1759857
Case Series

Catastrophic Antiphospholipid Syndrome: A Case Series

Navya Christopher 
1   Department of Radiology, Kovai Medical Center and Hospital, Coimbatore, India
,
Gopinath Periaswamy 
1   Department of Radiology, Kovai Medical Center and Hospital, Coimbatore, India
,
Venkatesh Kasi Arunachalam 
1   Department of Radiology, Kovai Medical Center and Hospital, Coimbatore, India
,
V. Mangalakumar
2   Department of Nephrology, Kovai Medical Center and Hospital, Coimbatore, India
,
Pankaj Mehta
1   Department of Radiology, Kovai Medical Center and Hospital, Coimbatore, India
,
Mathew Cherian
1   Department of Radiology, Kovai Medical Center and Hospital, Coimbatore, India
› Author Affiliations Funding None.
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Abstract

Catastrophic antiphospholipid syndrome (CAPS) is the rare but most severe form of antiphospholipid syndrome with multiple organ ischemia developing over a short period of time. CAPS should be considered when imaging suggests an acute and concurrent multiorgan ischemia, associated with positive antiphospholipid antibodies. As CAPS can have fulminant irreversible complications, its early recognition is important to initiate the treatment promptly. We present three patients of CAPS who were managed at our institution.

Keywords

antiphospholipid syndrome - CAPS - catastrophic antiphospholipid syndrome


Publication History

Article published online:
26 December 2022

© 2022. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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