Das Dandy-Walker-Syndrom

Das Dandy-Walker-Syndrom zählt zu den häufigsten angeborenen zerebellären Missbildungen. Hinter dieser Bezeichnung verbirgt sich aber eine Reihe verschiedener Krankheitsbilder mit ganz unterschiedlicher Pathologie, Therapie und Prognose. Der folgende Artikel bringt Licht in die verwirrende Terminologie, erleichtert die Diagnosestellung und hilft bei der Wahl der adäquaten Therapie entsprechend der zugrunde liegenden Malformation.

Schlüsselwörter

Dandy-Walker-Syndrom - Terminologie - Diagnostik - Therapie - Prognose

• Literatur

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