Gemischt epithelial-stromaler Tumor der Niere – Ein Fallbericht

Zusammenfassung

Ein gemischt epithelial-stromaler Tumor der Niere ist selten. Histologisch tritt er in einem Komplex aus Epithel und Stroma auf und enthält zystische und solide Areale. Prädisponiert sind vor allem perimenopausale Frauen mit Anwendung einer Hormonersatztherapie. Typische Symptome sind Hämaturie, Flankenschmerz und ein tastbarer Unterbauchtumor, wobei immer mehr Autoren über inzidentelle Tumoren berichten. So auch in unserem Fallbericht. Wir berichten über den ersten publizierten Fall in Deutschland: eine 60-jährige Patientin mit einem gemischt epithelial-stromalen Tumor der rechten Niere. Der Tumor wurde mittels laparoskopischer Nephrektomie entfernt.

Abstract

Mixed epithelial and stromal tumours of the kidney are rare. Histologically, they are characterised by a complex of epithelium and stroma with cystic and solid areas. They usually occur in perimenopausal women receiving hormone replacement with oestrogen. Typical symptoms are haematuria, flank pain and a palpable mass, with more and more authors reporting incidentally diagnosed tumours. This also applies to our case report. We are reporting the first published case in Germany: a 60-year-old female with a mixed epithelial and stromal tumour of the right kidney. The tumour was removed through complete nephrectomy.

Schlüsselwörter

Zentraler Nierentumor - komplizierte Nierenzysten - gemischt epithelial-stromaler Nierentumor

Keywords

Central tumour of the kidney - complex renal cysts - mixed epithelial and stromal tumour of the kidney

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