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CC BY-NC-ND 4.0 · Revista Chilena de Ortopedia y Traumatología 2023; 64(02): e109-e113
DOI: 10.1055/s-0043-1775833
Reporte de caso | Case Report

Case Report: Periosteal Ewing's sarcoma of the proximal humerus

Article in several languages: español | English
Hari Isvara Castro Herrán
1   Departamento de Ortopedia y Traumatología, Pontificia Universidad Católica de Chile, Santiago, Chile
,
María Emilia Riquelme Stagnaro
2   Facultad de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile
,
Tomás Zamora Helo
1   Departamento de Ortopedia y Traumatología, Pontificia Universidad Católica de Chile, Santiago, Chile
,
Laura Fonseca Muñoz
3   Departamento de Pediatría - Unidad Cuidados Intensivos, Pontificia Universidad Católica de Chile, Santiago, Chile
,
Eduardo Botello Correa
1   Departamento de Ortopedia y Traumatología, Pontificia Universidad Católica de Chile, Santiago, Chile
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Abstract

Ewing's sarcoma is the third most common malignant bone tumor, occurring in patients under 20 years of age in 80% of cases. Histologically it is composed of small round cells with round nuclei with chromatin and eosinophilic cytoplasm. For its definitive diagnosis, a molecular study is necessary. It classically affects the medullary cavity of the diaphysis of long bones, however, it has less frequent presentations such as the extra osseous and the periosteal. We present a case report of a 17-year-old patient with swelling in the left proximal humerus with imaging studies compatible with a periosteal tumor lesion that spares the medullary cavity. A biopsy of the tumor was performed with histopathological and molecular confirmation of Ewing's sarcoma, which was treated with concomitant chemotherapy and radiotherapy, obtaining a progressive decrease in the size of the lesion and therefore surgery was not necessary. Periosteal Ewing's sarcoma is an extremely unusual entity, with few cases reported in the literature, which makes it important to recognize and treat these aggressive bone lesions in a timely manner.

Keywords

ewing's sarcoma - parostal ewing's sarcoma - periostal ewing's sarcoma - sarcoma - bone tumor


Publication History

Received: 11 November 2022

Accepted: 14 August 2023

Article published online:
30 October 2023

© 2023. Sociedad Chilena de Ortopedia y Traumatologia. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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