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CC BY 4.0 · Indian Journal of Neurosurgery 2024; 13(02): 163-166
DOI: 10.1055/s-0043-1776360
Case Report

Spinal Epidural Hematoma Caused by Pure Epidural Spinal Arteriovenous Malformation: Case Report and Literature Review

Elisa Garbin 
1   Academic Neurosurgery, Department of Neurosciences, University of Padova, Padova, Italy
,
Nicola Cavasin
2   Department of Neurosciences, Ospedale dell'Angelo, Mestre, VE, Italy
,
Salima Magrini
2   Department of Neurosciences, Ospedale dell'Angelo, Mestre, VE, Italy
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Abstract

Spontaneous spinal epidural hematoma (SEH) represents an extremely rare cause of spinal cord compression. Symptomatic pure extradural spinal AVMs (E-sAVM), in the absence of cavernous hemangiomas, are very rare and have rarely been reported. The clinical presentation of SEH caused by E-sAVM is often nonspecific and may lead to delayed diagnosis and treatment. We report the case of a 16-year-old adolescent girl who presented with paraparesis that rapidly evolved in paraplegia. Emergent magnetic resonance imaging (MRI) of the whole spine showed a posterior SEH, extending from C7 to T2, highly suspicious for the presence of an underlying AVM. The patient underwent emergent C7–T2 laminoplasty. An E-sAVM was intraoperatively found and subsequently excised. The patient was discharged with no neurological defects. E-sAVMs are extremely rare pathologies; they represent an extremely rare cause of spinal cord compression. If immediately diagnosed and treated, most patients recover with good prognosis.

Keywords

epidural spinal hematoma - spinal epidural vascular malformation - spinal digital subtraction angiography


Publication History

Article published online:
23 November 2023

© 2023. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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