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CC BY 4.0 · Rev Bras Ortop (Sao Paulo) 2024; 59(S 02): e212-e215
DOI: 10.1055/s-0044-1779511
Relato de Caso

Reichel Syndrome in Children: A Case Report

Article in several languages: português | English
Hanene Lassoued Ferjani 
1   Departamento de Reumatologia, Kassab Orthopedics Institute, Ksar Saïd, Tunísia
2   Unidade de pesquisa UR17SP04, 2010, Ksar Said 2010, Tunis, Tunísia
,
Hiba Bettaib
1   Departamento de Reumatologia, Kassab Orthopedics Institute, Ksar Saïd, Tunísia
,
Ben Nessib Dorra
1   Departamento de Reumatologia, Kassab Orthopedics Institute, Ksar Saïd, Tunísia
2   Unidade de pesquisa UR17SP04, 2010, Ksar Said 2010, Tunis, Tunísia
,
Kaouther Maatallah
1   Departamento de Reumatologia, Kassab Orthopedics Institute, Ksar Saïd, Tunísia
2   Unidade de pesquisa UR17SP04, 2010, Ksar Said 2010, Tunis, Tunísia
,
Mourad Jenzri
2   Unidade de pesquisa UR17SP04, 2010, Ksar Said 2010, Tunis, Tunísia
3   Departamento de Ortopedia Pediátrica, Kassab Orthopedics Institute, Ksar Saïd, Tunísia
,
Wafa Hamdi
1   Departamento de Reumatologia, Kassab Orthopedics Institute, Ksar Saïd, Tunísia
2   Unidade de pesquisa UR17SP04, 2010, Ksar Said 2010, Tunis, Tunísia
› Author Affiliations Financial Support The authors declare that the present research did not receive any specific grant from funding agencies in the public, commercial, or notfor-profit sectors.
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Abstract

Reichel syndrome or primary synovial chondromatosis (PSC) is an uncommon benign metaplastic condition that usually affects large joints. Though shoulder involvement was scarce, there are only a few cases in the pediatric population. A 14- year-old boy was admitted to the Pediatric Orthopedics department with right shoulder pain for 14 months. Imaging revealed multiple loose bodies distributed throughout the glenohumeral joint. Upon the arthroscopic approach, we remove all cartilaginous nodules within the glenohumeral space and abarticular tendon. Histopathologic examination confirmed the diagnosis of primary synovial chondromatosis. At follow-up, the patient remains free of symptoms, and shoulder radiographs showed no recurrence of calcification. The present case illustrates the clinical patterns, imaging features, histological findings, and therapeutic management of shoulder primary synovial chondromatosis in a pediatric patient.

Keywords

chondromatosis - pediatrics - shoulder - synovial

Work carried out at the Kassab Orthopedics Institute, Mannouba, Tunisia.




Publication History

Received: 10 August 2022

Accepted: 15 September 2022

Article published online:
27 December 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution 4.0 International License, permitting copying and reproduction so long as the original work is given appropriate credit (https://creativecommons.org/licenses/by/4.0/)

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