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CC BY 4.0 · Rev Bras Ortop (Sao Paulo) 2024; 59(S 02): e216-e219
DOI: 10.1055/s-0044-1790594
Relato de Caso

Surgical Excision of a Hemophilic Pseudotumor Causing Vascular Impingement in a Patient with Severe Hemophilia A: A Case Report

Article in several languages: português | English
Juan Manuel Pradilla 
1   Departamento de Cirurgia Ortopédica, Fundación Cardioinfantil, Instituto de Cardiología, Bogotá, Colômbia
,
Abelardo Tinoco 
1   Departamento de Cirurgia Ortopédica, Fundación Cardioinfantil, Instituto de Cardiología, Bogotá, Colômbia
,
Luis Miguel Cely 
1   Departamento de Cirurgia Ortopédica, Fundación Cardioinfantil, Instituto de Cardiología, Bogotá, Colômbia
,
Martha Paola Buitrago 
1   Departamento de Cirurgia Ortopédica, Fundación Cardioinfantil, Instituto de Cardiología, Bogotá, Colômbia
› Author Affiliations Financial Support The authors declare that there was no financial support from public, commercial, or non-profit sources.
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Abstract

Patients with hemophilia disease have a high risk of hemorrhage. Most hemorrhages can occur in the musculoskeletal system, presenting as hematomas, or, in rare occasions, as hemophilic pseudotumors, an uncommon pathology that are often misdiagnosed as musculoskeletal tumors because of their clinical behavior and characteristics on diagnostic imaging. Despite many treatment options, surgical excision is the treatment of choice. This article describes a case of hemophilia A in a patient who suffered from progressive swelling of the right thigh for 12 months. Diagnostic imaging suggested a hemophilia pseudotumor with vascular bundle impingement. Surgical excision was successful.

Keywords

hematoma - hemophilia A - hemorrhage - musculoskeletal system

Work carried out at the Department of Orthopedic Surgery, Fundación Cardioinfantil, Instituto de Cardiología, Bogotá, Colombia.




Publication History

Received: 03 July 2023

Accepted: 25 August 2023

Article published online:
27 December 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution 4.0 International License, permitting copying and reproduction so long as the original work is given appropriate credit (https://creativecommons.org/licenses/by/4.0/)

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