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CC BY-NC-ND 4.0 · Asian J Neurosurg
DOI: 10.1055/s-0044-1791581
Case Report

Nonenhancing Prepontine Chordoma with Diffusion Restriction Mimicking an Epidermoid Cyst

Bheru Dan Charan 
1   Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India
4   Department of Diagnostic and Interventional Radiology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
,
Sushant Agarwal
5   Department of Radio-Diagnosis, All India Institute of Medical Sciences, Guwahti, Assam, India
,
Ekamjot Singh
1   Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India
,
Savyasachi Jain
1   Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India
,
Sumanta Das
2   Department of Neuropathology, All India Institute of Medical Sciences, New Delhi, India
,
Ajay Garg
1   Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India
,
Leve Joseph Devarajan Sebastian
1   Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India
,
Manmohan Singh
3   Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India
› Author Affiliations Funding None.
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Abstract

Intradural prepontine chordoma is an extremely rare entity and depicts benign features with no recurrence and has a good prognosis as compared with bone endogenous chordoma. Radiologically, it may mimic an epidermoid cyst and present an imaging challenge. Here we present a case of a middle adolescent girl who presented with headache along with limb and facial weakness. A nonenhancing, diffusion-restricting, predominantly intradural cystic-appearing mass lesion was seen in the prepontine cistern. Initially, an epidermoid cyst was suspected, but histopathology revealed it to be a chordoma. Destruction of the clivus is important and chordoma should be included in differential diagnosis.

Keywords

chordoma - epidermoid cyst - diffusion restriction

Authors' Contributions

B.D.C., S.A., S.D., E.S., S.J., A.G., L.J.D.S., and M.S. contributed to the acquisition, analysis, conception, design, and drafting of the work. B.D.C. and E.S., along with A.G. and L.J.D.S., contributed to the final draft, revisions, upload, and submission of the final revised work. All the authors have agreed both to be personally accountable for their contributions and to ensure that questions related to the accuracy or integrity of any part of the work, even ones in which one was not personally involved, are appropriately investigated and resolved, and the resolution documented in the literature. All the authors have read and approved the manuscript.


Patients' Consent

Written informed consent to publish this information was obtained from study participants.




Publication History

Article published online:
10 October 2024

© 2024. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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