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CC BY-NC-ND 4.0 · Asian J Neurosurg
DOI: 10.1055/s-0044-1791948
Case Report

Persistent Craniopharyngeal Canal (Type 3C) with Vertebrobasilar Dolichoectasia and Bilateral Sclerochoroidal Calcification

Bheru Dan Charan 
1   Department of Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India
2   Department of Radio-diagnosis, All India Institute of Medical Sciences, Rishikesh, Rishikesh, Uttarakhand, India
,
Savyasachi Jain
1   Department of Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India
,
Shailesh B. Gaikwad
1   Department of Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India
› Author Affiliations Funding Retrospective, consent waiver, adhered to Helsinki guidelines.
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Abstract

The persistent craniopharyngeal canal is a rare, well-corticated midline congenital bony defect through the sphenoid bone between the sellar floor and the nasopharyngeal roof. The prevalence of persistent craniopharyngeal canal is reported to be 0.42%. A 42-year-old male was evaluated for nasal discharge and progressive vision loss; and underwent computed tomography and magnetic resonance imaging, which revealed a large craniopharyngeal canal with ectopic pituitary, lipoma, encephalocele, deformed globe with sclerochoroidal calcification and vertebrobasilar dolichoectasia. The presence of orbital and optic tract malformation, craniofacial anomalies, and tumors can be associated with the craniopharyngeal canal.

Keywords

cephalocele - lipoma - craniopharyngeal canal

Note

A part of the history and images of this patient are published along with other cases series in the original article (DOI: 10.25259/JCIS_87_2023) from the same institute and corresponding author. Here, we want to publish more elaborative literature regarding this anomaly.


Authors' Contributions

B.D.C., S.J., and S.B.G. contributed to the acquisition, analysis, conception, design, and drafting of the work. All authors have agreed both to be personally accountable for their contributions and ensured that questions related to the accuracy or integrity of any part of the work, even ones in which one was not personally involved, are appropriately investigated, resolved, and the resolution documented in the literature. All authors have read and approved the manuscript.




Publication History

Article published online:
22 October 2024

© 2024. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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