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DOI: 10.1055/s-0045-1802669
Type 2 Congenital Pulmonary Airway Malformation in Tetralogy of Fallot with Absent Pulmonary Valve Syndrome
Abstract
Tetralogy of Fallot with absent pulmonary valve syndrome is a unique congenital condition often accompanied with dilated pulmonary arteries causing varied degree of airway compression. Frequently, abnormal pulmonary arterial branching at the segmental level and compression at the level of intrapulmonary bronchi can be seen. The occurrence of isolated bronchopulmonary malinosculation in the form of congenital pulmonary airway malformation is exceedingly rare. This report highlights a case of such rarity, involving a young child with recurrent lower respiratory tract infections.
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Informed consent was taken from the concerned patient.
Publication History
Article published online:
27 March 2025
© 2025. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)
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