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CC BY-NC-ND 4.0 · Asian J Neurosurg
DOI: 10.1055/s-0045-1805088
Case Report

Utility of Intraoperative Ultrasound in Surgical Management of Lhermitte–Duclos Disease: A Case Report

Parth Parikh 
1   Department of Neurosurgery, Lokmanya Tilak Municipal General Hospital, Mumbai, Maharashtra, India
,
Naren Nayak
1   Department of Neurosurgery, Lokmanya Tilak Municipal General Hospital, Mumbai, Maharashtra, India
,
Shubham Goyal
1   Department of Neurosurgery, Lokmanya Tilak Municipal General Hospital, Mumbai, Maharashtra, India
,
Neelanjana Ghosh
2   Department of General Surgery, Pandit Deen Dayal Upadhyay Medical College, Rajkot, Gujarat, India
,
Rahul Pandey 
1   Department of Neurosurgery, Lokmanya Tilak Municipal General Hospital, Mumbai, Maharashtra, India
› Institutsangaben Funding None.
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Abstract

Lhermitte–Duclos disease (LDD) is a rare, autosomal dominant, dysplastic gangliocytoma of the cerebellum. It is a slow-growing benign tumor. The challenges in the surgical resection of these tumors lie in accurately delineating the tumor margin from the normal cerebellar parenchyma. Intraoperative ultrasound has the potential to overcome these limitations. A 30-year-old woman was diagnosed as having LDD showing a typical “tigroid” appearance on MRI. Intraoperative ultrasound was used to delineate the tumor margins and near-total resection was done via right suboccipital craniectomy. The diagnosis was confirmed on histopathological examination. Postoperatively there were no neurological deficits, and the patient is on regular follow-up for screening of Cowden's syndrome. We report this case to highlight the undervalued utility of intraoperative ultrasonography while dealing with patients with LDD. This modality serves as an effective tool to maximize the extent of resection without adding to postoperative morbidity.

Keywords

Lhermitte–Duclos disease - dysplastic gangliocytoma - Cowden's syndrome - intraoperative ultrasound - tigroid appearance


Publikationsverlauf

Artikel online veröffentlicht:
18. März 2025

© 2025. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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