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Semin Liver Dis 2001; 21(1): 115-118
DOI: 10.1055/s-2001-12934
Diagnostic Problems in Hepatology
Copyright © 2001 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA. Tel.: +1(212) 584-4662

Hepatic Weber-Christian Disease

Jared M. Wasserman2 , Swan N. Thung3 , Richard Berman4 , Henry C. Bodenheimer, Jr.1,2 , Samuel H. Sigal1,2
  • 1Division of Liver Diseases, Mount Sinai School of Medicine of New York University, New York, NY
  • 2Department of Medicine, Mount Sinai School of Medicine of New York University, New York, NY
  • 3Department of Pathology, Mount Sinai School of Medicine of New York University, New York, NY
  • 4Brookhaven Memorial Hospital Medical Center, Patchogue, NY
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Publikationsdatum:
31. Dezember 2001 (online)

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ABSTRACT

Weber-Christian disease is an idiopathic disorder characterized by nonsuppurative nodular panniculitis with a lobular distribution of acute inflammation in the subcutaneous fat with occasional systemic involvement. Although the histopathologic features of the liver disease in the syndrome are characterized by steatohepatitis, the clinical features have not been well defined. We report a case of hepatic Weber-Christian disease and discuss the clinical differences from steatohepatitis due to the more common disorders of obesity and diabetes mellitus.

KEYWORD

Weber-Christian disease - steatohepatitis - liver

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