Solid-pseudopapillärer Pankreastumor im Kindesalter

Zusammenfassung

Wir berichten über 5 Patientinnen mit einem solid-pseudopapillären Tumor des Pankreas. Diese Tumoren sind im Kindesalter selten. Mädchen werden deutlich häufiger befallen als Jungen. Der Malignitätsgrad ist niedrig. Eine Metastasierung, meist in die Leber oder das Peritoneum, kommt nur selten vor. Die zum Zeitpunkt der Diagnosestellung oft sehr großen Tumoren sind fast immer vollständig resektabel. Die Prognose gilt danach als gut. Die Abgrenzung gegen andere Pankreastumoren ist deshalb von Bedeutung.

Abstract

We report on fife female patients with solid pseudopapillary tumors of the pancreas. The tumors are extremely rare in children. They occur mainly in adolescent and young adult females. The tumors are neoplasms of low malignancy with infrequent metastases, for instance, in the liver or the peritoneum. Although the tumors had reached a large diameter, all of them underwent complete tumor resection. After that the patients have a very good prognosis. Thus, so it is important to distinguish solid-pseudopapillary tumors from other tumors of the pancreas.

Schlüsselwörter

Solid-pseudopapillärer Tumor - Pankreas - Papillär-zystischer Tumor - Therapie - Prognose

Key words

Solid-pseuodpapillary tumor - Pancreas - Papillary cystic tumor - Therapy - Prognosis

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