Here, we report on a case of coronary artery fistula that developed following the repair of a double-outlet right ventricle (DORV) with infundibular pulmonary stenosis in a patient who has a single coronary artery. The major concern in this case was that of reduction of coronary blood flow from the patient's only coronary artery to the myocardium distal to the fistula.
Coronary artery fistula - Double-outlet right ventricle - Single coronary artery