A Particular Case with Long-Term Follow-Up of Rare malignant Hemangiopericytoma of the Lung with Metachronous Diaphragmatic Metastasis

P. P. Brega Massone; C. Lequaglie; B. Conti; F. Ferro; B. Magnani; I. Cataldo

doi:10.1055/s-2002-32407

The Thoracic and Cardiovascular Surgeon, Table of Contents

Thorac Cardiovasc Surg 2002; 50(3): 178-180
DOI: 10.1055/s-2002-32407

Case Report

A Particular Case with Long-Term Follow-Up of Rare malignant Hemangiopericytoma of the Lung with Metachronous Diaphragmatic Metastasis

P. P. Brega Massone¹ , C. Lequaglie¹ , B. Conti¹ , F. Ferro² , B. Magnani³ , I. Cataldo¹

¹Oncologic Thoracic Surgery, Istituto Nazionale Tumori, Milan, Italy
²General Surgery, Ospedale Civile, Voghera, Italy
³Statistical Unit IIAARR, Pavia, (Italy)

The work was performed at Instituto Nazionale Tumori, Via Venezian 1, Milan, Italy. The abstract was presented at the 9th Congress of the European Society of Surgical Oncology (ESSO), Lausanne (Switzerland), June 3 - 6, 1998.

Abstract

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Abstract

The authors report the case of a woman with a primary hemangiopericytoma of the lung and successive metachronous diaphragmatic metastasis treated with surgery only according to the patient’s decision. The patient was first submitted to left lower lobectomy with resection of diaphragm and three ribs en-bloc for pulmonary sarcoma. One year later, a chest computed tomography (CT) scan showed a small lesion above the diaphragm on the left side. She refused the proposed operation and returned fifteen months later with a new thorax CT, and told us that she had in the meantime become pregnant and given birth. A rethoracotomy to remove the metastatic diaphragmatic tumor was performed. Chemotherapy with anthracycline and iphosphamide was proposed, but the patient again refused therapy for fear of side effects impairing another pregnancy. Currently, the patient is alive and disease-free, 68 months after the first treatment. The authors emphasize the long-term follow-up obtained with surgery alone in this kind of rare sarcoma.

Key words

Soft tissue sarcoma - Hemangiopericytoma - Pulmonary surgery - Diaphragmatic metastasis

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References

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Correspondence

Pier Paolo Brega MassoneMD

Via Cascina Spelta 24/b

27100 Pavia

Italy

Phone: +39 (2) 239 023 84

Fax: +39 (2) 236 04 86

Email: ppbm@virgilio.it