Angioendotheliomatose

Zusammenfassung

Wir berichten über eine 57-jährige Patientin mit multiplen livid-roten Hautinfiltraten im Bereich beider Ohrhelices. Die Diagnose einer reaktiven Angioendotheliomatose wurde histologisch, immunhistologisch und elektronenmikroskopisch anhand proliferierender Endothelzellen mit intravasalen Fibrinthromben gestellt. Verschiedenste Therapieansätze konnten die Erkrankung bei nicht nachweisbarer Grund- bzw. Begleiterkrankung nur mäßig beeinflussen. Wir geben eine Literaturübersicht zur benignen und malignen Form der Angioendotheliomatose.

Abstract

We report about a 57-year-old female patient with multiple livid red skin infiltrations in the area of both ear helices. A reactive angioendotheliomatosis was diagnosed histologically, immunhistologically and by means of electron microscopy showing proliferating endothelial cells with intravasal fibrin thrombus. Different therapeutic concepts could not influence the course of the disease distinctly as the primary or accompanying illness could not be found. We give a review of literature regarding benign and malignant forms of angioendotheliomatosis.

Literatur

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