Intracerebral Inflammatory Pseudotumour in a 16-Month-Old Boy

Abstract

A 16-month-old boy presenting with a previous two-month history of absences, was admitted for partial seizures and vomiting. Magnetic resonance imaging revealed a left temporo-occipital intraparenchymatous, well circumscribed lesion. Complete macroscopic resection was performed. Morphological and immunohistochemical analyses were conclusive for an inflammatory pseudotumour. Only a few cases of intracranial locations of this entity have been reported. Our case is the first described in an infant younger than four years of age. This observation suggests that chronic evolution may start earlier than thought in adult cases, perhaps due to an autoimmune process.

Key words

Inflammatory pseudotumour - inflammatory myofibrohistiocytic tumour - plasma cell granuloma - brain - infant - pathology

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