Solid-pseudopapillary Tumor of the Pancreas and Endoscopic Ultrasound

Zusammenfassung

Beim solide-pseudopapillären Pankreastumor (SPT) handelt es sich um eine sehr seltene Neoplasie, die überwiegend junge Mädchen befällt. Obwohl die Erstbeschreibung bereits 1959 durch Frantz erfolgte, wurde diese Tumorentität erst 1996 in die WHO-Klassifikation der exokrinen Pankreastumoren aufgenommen. Diese Tumoren werden als seltene, niedrigmaligne Geschwülste eingestuft. Anhand eines Falls bei einem 12-jährigen Jungen wird das endosonographische Bild dargestellt.

Abstract

The solid-pseudopapillary tumor of the pancreas (SPT) is an unusual epithelial tumor affecting predominantly adolescent young girls. The first original description by Frantz was in 1959 and in 1996 it was introduced in the World Health Organization (WHO) classification of tumors of the exocrine pancreas. These tumors have been reported as rare lesion with low malignant potential. In our case report of a 12-year old boy we show the feature of endoscopic ultrasound.

Schlüsselwörter

Solid-pseudopapillärer Tumor - Endosonographie - duodenumerhaltende Pankreasteilresektion

Key words

Solid-pseudopapillary tumor - endoscopic ultrasound - duodenum-sparing pancreaticoduodenectomy

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