A 68-year-old woman with progressive visual loss and exophthalmos in her right eye had been operated on for a mass in her right calf 3 years earlier. Imaging showed a huge mass invading the orbital structures and temporal pole. The presumptive diagnosis was a malignant orbital tumor. The tumor was resected totally and eroded tissues such as the lateral rectus muscle and dural compartments were repaired. The histological diagnosis was a malignant peripheral nerve sheath tumor (MPNST). The patient recovered uneventfully and was discharged 8 days after surgery. Two years later she died from a liver tumor. Few MPNSTs involving the orbit have been reported.
KEYWORDS
Malignant peripheral nerve sheath tumor - orbit
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Dr
Mehmet D Aydin
Atatürk Üniversitesi Lojmanlari
60 Blok, Kat 1, No. 3, Erzurum, Turkey
Email: nmda21@hotmail.com
