Thorac Cardiovasc Surg 2005; 53(4): 259-260
DOI: 10.1055/s-2005-865603
Short Communication

© Georg Thieme Verlag KG Stuttgart · New York

A Giant Rhabdomyoma with Left Ventricular Inflow Occlusion and Univentricular Physiology

U. Abdel-Rahman1 , F. Özaslan1 , A. Esmaeili2 , A. Moritz1
  • 1Department for Thoracic and Cardiovascular Surgery, Johann Wolfgang Goethe University, Frankfurt/Main, Germany
  • 2Department for Pediatric Cardiology, Johann Wolfgang Goethe University, Frankfurt/Main, Germany
Further Information

Publication History

Received January 6, 2005

Publication Date:
22 July 2005 (online)

Abstract

During a routine prenatal ultrasound a huge tumor was diagnosed located in the left ventricle and left atrium with complete obstruction of the left ventricular inflow tract. On the first day of life, urgent surgical intervention was necessary because of progressive heart failure with univentricular physiology. Intraoperatively, the tumor mass was found to originate from the left ventricular wall, reaching into the left atrium. Histological examination revealed a rhabdomyoma.

References

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MD Ulf Abdel-Rahman

Thoracic and Cardiovascular Surgery
Johann Wolfgang Goethe University

Theodor-Stern-Kai 7

60590 Frankfurt am Main

Germany

Phone: + 496963016141

Fax: + 49 69 63 01 58 49

Email: abdel-rahman@em.uni-frankfurt.de