A Giant Rhabdomyoma with Left Ventricular Inflow Occlusion and Univentricular Physiology

Abstract

During a routine prenatal ultrasound a huge tumor was diagnosed located in the left ventricle and left atrium with complete obstruction of the left ventricular inflow tract. On the first day of life, urgent surgical intervention was necessary because of progressive heart failure with univentricular physiology. Intraoperatively, the tumor mass was found to originate from the left ventricular wall, reaching into the left atrium. Histological examination revealed a rhabdomyoma.

Rhabdomyoma - univentricular physiology - congenital heart disease

References

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