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DOI: 10.1055/s-2006-924485
© Georg Thieme Verlag KG Stuttgart · New York
Aortic Valve Replacement in an Adult 20 Years after a Single-Stage Extra-Anatomic Repair of an Interrupted Aortic Arch
Publication History
Received June 2, 2006
Publication Date:
05 April 2007 (online)
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Introduction
Interrupted aortic arch is a rare congenital malformation that occurs in 3 cases per million [[1]]. This anomaly is defined as a loss of luminal continuity between the ascending and the descending aorta, and there is usually a considerable distance between the ascending and descending parts of the aorta [[2]]. A classification system, based on the location of the interrupted segment, was introduced by Celoria and Patton in 1959. In type A (30 - 40 %), the interruption lies distal to the left subclavian artery. Type B (53 %) is the most common type with an interruption between the left subclavian artery and the left common carotid artery. In rare type C (4 %), the interruption is proximal to the left common carotid artery. The natural history is very poor, 80 % of children die within the first month if untreated [[3]].
We describe a single-stage, extra-anatomic repair in an adolescent patient with a type C interrupted aortic arch and his subsequent aortic valve replacement 19 years later.
References
- 1 Conova C R, Carrel T, Dubach P, Turina M, Reinhart W H. Interrupted aortic arch: fortuitous diagnosis in a 72-year-old female patient with severe aortic insufficiency [in German]. Schweiz Med Wochenschr. 1995; 125 26-30
- 2 Backer C L, Mavroudis C. Congenital Heart Surgery Nomenclature and Database Project: patent ductus arteriosus, coarctation of the aorta, interrupted aortic arch. Ann Thorac Surg. 2000; 69 (Suppl 4) S298-S307
- 3 Celoria G C, Patton R B. Congenital absence of the aortic arch. Am Heart J. 1959; 58 407-413
- 4 Goldmuntz E, Clark B J, Mitchel L E, Jawad A F, Cuneo B F, Reed L. Frequency of 22q11 deletions in patients with conotruncal defects. J Am Coll Cardiol. 1998; 32 492-498
Dr. Daniela Martin
Division of Cardiac Surgery
Medical School of Graz
Auenbruggerplatz 29
8036 Graz
Austria
Fax: + 43 31 63 85 46 72
Email: daniela-eugenia.martin@meduni-graz.at