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Semin Thromb Hemost 2006; 32(3): 171-173
DOI: 10.1055/s-2006-939430
Copyright © 2006 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA.

Epidemiology of the Myeloproliferative Disorders Polycythemia Vera and Essential Thrombocythemia

Peter Johansson1
  • 1Associate Professor, Department of Hematology, Sahlgrenska University Hospital, Göteborg, Sweden
Further Information

Publication History

Publication Date:
02 May 2006 (online)

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ABSTRACT

The annual incidence of polycythemia vera (PV) and essential thrombocythemia (ET) is ~2 and 1.5 per 100,000 inhabitants, respectively, if based on large population surveys and adjusted to a standard population. Survival for ET patients does not differ from that of the general population. However, it appears that PV patients have a significantly higher mortality, at least for patients diagnosed before 1990.

KEYWORDS

Polycythemia vera - essential thrombocythemia - incidence - mortality - survival

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 Dr.
Peter Johansson

Department of Hematology, Sahlgrenska University Hospital

S-41345 Göteborg, Sweden

Email: peter.l.johansson@vgregion.se