Epidemiology of the Myeloproliferative Disorders Polycythemia Vera and Essential Thrombocythemia

ABSTRACT

The annual incidence of polycythemia vera (PV) and essential thrombocythemia (ET) is ~2 and 1.5 per 100,000 inhabitants, respectively, if based on large population surveys and adjusted to a standard population. Survival for ET patients does not differ from that of the general population. However, it appears that PV patients have a significantly higher mortality, at least for patients diagnosed before 1990.

KEYWORDS

Polycythemia vera - essential thrombocythemia - incidence - mortality - survival

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