Left-Ventricular Inflow Obstruction Due To a Dilated Coronary Sinus Mimicking Cor Triatriatum

Abstract

Persistence of the left superior vena cava with drainage to the coronary sinus is a common congenital anomaly. We report an infant with such a malformation associated with marked enlargement of the coronary sinus, which produced partial supramitral obstruction and consequently impairment to the left-ventricular inflow. The patient presented with cardiac failure in infancy and features mimicking cor triatriatum. Surgical relief of the supramitral obstruction resulted in immediate reversal of the pulmonary hypertension, with clinica! improvement. This rare entity, only once previously reported, is an unusual cause of pulmonary hypertension in infancy.

Key words

Coronary sinus - Left superior vena cava - Pulmonary hypertension