Aortitis with involvement of the aortic valve is rarely associated with vasculitis Syndromes. We present a patient with antibodies to a neutrophil cytoplasmic antigen-associated (ANCA) vasculitis with renal failure who developed aortic incompetence as a result of aortitis which involved the aortic valve. Thickening of the aortic wall also caused Stenosis of the left coronary ostium.
Aortitis - Aortic incompetence - Coronary ostium Stenosis - ANCA associated vasculitis - Wegener's granulomatosis