Cutis Verticis Gyrata Associated with Periventricular Calcifications

Introduction

Cutis verticis gyrata (CVG) is an unusual abnormality of the scalp characterized by the formation of folds and furrows that typically cannot be corrected by pressure or traction. Such morphological alteration is referred to variously in dermatological literature as “bull-dog scalp”, “cutis sulcata” “corrugated skin”, or Robert-Unna syndrome (Striano S et al. Epilepsia 1996; 37: 284).

The purpose of this case report is two-fold: to familiarize the radiologist with the imaging features of this rare pathological process and to report the unusual association with intracranial periventricular calcifications which has never been reported before.