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Neuropediatrics 1995; 26(4): 220-222
DOI: 10.1055/s-2007-979759
Short communications

© Hippokrates Verlag GmbH Stuttgart

Sturge-Weber Syndrome Without Facial Nevus

I. Pascual-Castroviejo1 , S.-I. Pascual-Pascual1 , J. Viaño2 , V. Martinez2 , J. Coya3
  • 1Service of Pediatric Neurology, Hospital Infantil "La Paz", Madrid,
  • 2Unity of Imaging, Sanatorio Nuestra Sefiora del Rosario, Madrid,
  • 3Service of Nuclear Medicine, Hospital "La Paz", Madrid, Spain
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Publication History

Publication Date:
19 April 2007 (online)

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Abstract

A patient with Sturge-Weber syndrome without the characteristic facial nevus presented with focal seizures which were difficult to control and borderline mental level. CT disclosed calcification in the right occipital zone. A marked decrease of the regional cerebral blood flow that extended beyond the abnormalities depicted on CTwas seen by SPECT. Venous magnetic resonance (MR) angiography revealed reduction of the superficial cortical veins and prominent deep collateral venous system in the same side of the cerebral lesion. Cranial MR imaging with Gd-DTPA demonstrated the pial angioma.

Key words

CT - Epilepsy - MR - MR angiography - MR with Gd-DTPA - SPECT - Sturge-Weber syndrome