Evaluating Infants and Children with Interstitial Lung Disease

Robin Deterding

doi:10.1055/s-2007-981654

Seminars in Respiratory and Critical Care Medicine, Inhaltsverzeichnis

Semin Respir Crit Care Med 2007; 28(3): 333-341
DOI: 10.1055/s-2007-981654

Evaluating Infants and Children with Interstitial Lung Disease

Robin Deterding¹

¹Department of Pediatrics, University of Colorado, School of Medicine, The Children's Hospital, Denver Colorado

Abstract

ABSTRACT

The field of children's interstitial lung disease (chILD) has been confusing for clinicians and families. It is fraught with imperfect pediatric definitions and classification systems, limited understanding of underlying molecular mechanisms, pathophysiology and natural history, and inadequate clinical networks to improve care. To address these issues two large efforts have focused on chILD: a European Respiratory Society (ERS) Task Force on chronic interstitial lung disease in children[1] and the National Institute of Health (NIH)-sponsored Rare Lung Disease Consortium (RLDC). Collaborative efforts in chILD research have retrospectively studied large numbers of children with ILD using different strategies. Both efforts have yielded new concepts and approaches to the evaluation of pediatric patients with ILD. Diagnostic techniques have also evolved to provide more advanced testing in children. This article reviews the current evaluation for children with ILD and highlights areas of controversy.

KEYWORDS

Pediatric - interstitial - children's interstitial lung disease (chILD) - diffuse lung disease

Volltext

Referenzen

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Robin DeterdingM.D.

Department of Pediatrics, University of Colorado, School of Medicine, The Children's Hospital

1056 E. 19th Ave., Box 395, Denver, CO 80218

eMail: deterding.robin@tchden.org