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Cent Eur Neurosurg 2008; 69(1): 47-50
DOI: 10.1055/s-2007-985162
Case Report

© Georg Thieme Verlag KG Stuttgart · New York

Gangliocytic Paraganglioma of the Cauda Equina with Significant Calcification: First Description in Pediatric Age

Gangliozytisches Paragangliom der Cauda Equina mit kräftiger Verkalkung: Erstbeschreibung im KindesalterM. Vural 1 , A. Arslantas 1 , S. Isiksoy 2 , B. Adapinar 3 , M. Atasoy 1 , F. Soylemezoglu 4
  • 1Department of Neurosurgery, School of Medicine, Eskisehir Osmangazi University, Eskisehir, Turkey
  • 2Department of Pathology, School of Medicine, Eskisehir Osmangazi University, Eskisehir, Turkey
  • 3Department of Radiology, School of Medicine, Eskisehir Osmangazi University, Eskisehir, Turkey
  • 4Department of Pathology, School of Medicine, Hacettepe University, Ankara, Turkey
Further Information

Publication History

Publication Date:
21 January 2008 (online)

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Abstract

A 17-year-old boy was referred with a 2-month history of low back pain and bilateral sciatica and difficulty in ambulation. Neurological examination found mild muscle weakness and diminished deep tendon reflexes in his right leg. Lumbar magnetic resonance imaging revealed an intradural-extramedullary tumor at the level of the L4, exiting through the right L4-L5 intervertebral foramen into the right psoas muscle. After total resection of the tumor, histopathological diagnosis revealed a gangliocytic paraganglioma. There are 184 paraganglioma cases reported at the lumbar region to date, and only 4 of them were in the pediatric age group. This report is the fifth paraganglioma case in the lumbar region and the first gangliocytic paraganglioma case in the pediatric age population.

Zusammenfassung

Ein 17-jähriger Patient wurde mit seit zwei Monaten andauernden Rückenschmerzen und beidseitigen Ischiasbeschwerden in die Klinik eingewiesen, Bei der neurologischen Untersuchung fand sich eine leichte Schwäche am rechten Bein und ein Verlust der Muskeleigenreflexe. Im lumbalen MRT wurde in der Höhe L4/5 ein im Intervertebralforamen wachsender und in den rechten Psoasmuskel übergreifender intra-/extramedullärer Tumor festgestellt. Der Tumor wurde total entfernt und nach der histopathologischen Untersuchung als gangliozytisches Paragangliom beschrieben. In der Literatur sind bisher in der Lumbalregion 184 Paragangliome beschrieben und nur vier gehörten in die pädiatrische Altersgruppe. Dieser Report schildert das fünfte Paragangliom in der Lumbalregion und das erste gangliozytische Paragangliom in der pädiatrischen Altersgruppe.

Key words

spinal tumor - paraganglioma - gangliocytic paraganglioma - pediatric age - extradural extension - calcification

Schlüsselwörter

spinaler Tumor - Paragangliom - gangliozytisches Paragangliom - Kindesalter - extradurale Verkalkung

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Correspondence

Dr. M. Vural

Department of Neurosurgery

School of Medicine

Eskisehir Osmangazi University

Deliklitas Mh. Deliklitas Cd. Huzur Apt., No 30/3

26000 Eskisehir

Turkey

Phone: +90/222/234 19 06

Fax: +90/222/239 22 20

Email: mvural@ogu.edu.tr