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DOI: 10.1055/s-2007-989281
© Georg Thieme Verlag KG Stuttgart · New York
Papillary Fibroelastomas of the Heart
Publication History
received July 10, 2007
Publication Date:
17 January 2008 (online)
![](https://www.thieme-connect.de/media/thoracic/200801/lookinside/thumbnails/10.1055-s-2007-989281-1.jpg)
Abstract
Cardiac papillary fibroelastomas (CPFs), the second most common primary cardiac tumor, are benign endocardial papillomas predominantly affecting the cardiac valves. Although CPFs are rare and benign tumors, they may result in life-threatening complications. Early diagnosis of this condition is important, since it represents a surgically correctable cause of systemic embolism, myocardial infarction, stroke, acute valve dysfunction, and sudden cardiac death. This review summarizes the significance and clinical approach for the diagnosis of this cardiac entity. The differential diagnosis, histological characteristics of CPF and current treatment strategies are also discussed.
Key words
cardiovascular surgery - heart valve surgery - heart tumors - papillary fibroelastoma
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Dr. MD Karsten Sydow
Department of Cardiology
Hamburg University Heart Center
Martinistraße 52
20246 Hamburg
Germany
Phone: + 49 4 04 28 03 88 64
Fax: + 49 4 04 28 03 88 62
Email: sydow@uke.de