Askin's Tumor: A Rare Chest Wall Neoplasm. Case Report and Short Review

Introduction

Askin's tumor is an uncommon, malignant, small round cell tumor which belongs to the Ewing's sarcoma family of tumors (ESFT) [[1]]. More specifically, it is a peripheral primitive neuroectodermal tumor (PNET) located exclusively in the thoracopulmonary region, which was first described in childhood by Askin et al. in 1979 [[2]]. The prognosis is usually dismal with extremely low 6-year survival rates [[3]]. However, very few cases have been reported with good long-term survival rates [[1], [4]]. We present here a patient with an Askin's tumor, who was treated satisfactorily with aggressive multimodal treatment. The patient has not suffered any recurrence at the time when this report was written. This is the first, well documented case of Askin's tumor in Greece. Especial emphasis is placed on the immunohistological features and the currently established therapeutic regimen for this rare entity.

References

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