Thorac Cardiovasc Surg 2008; 56(7): 430-432
DOI: 10.1055/s-2007-989367
Short Communications

© Georg Thieme Verlag KG Stuttgart · New York

Tetralogy of Fallot and Absence of Left Pulmonary Artery

V. Halit1 , R. Olguntürk2 , D. Erer1 , S. Kula2
  • 1Department of Cardiovascular Surgery, Gazi University Medical School, Ankara, Turkey
  • 2Department of Pediatric Cardiology, Gazi University Medical School, Ankara, Turkey
Further Information

Publication History

Received October 5, 2007

Publication Date:
22 September 2008 (online)

Introduction

Unilateral absence of the pulmonary artery (UAPA) is a rare congenital lesion with a diverse clinical presentation [1]. More frequently, UAPA is associated with severe cardiovascular anomalies such as tetralogy of Fallot (TOF) or septal defects. There are few reports in the literature describing such a dilemma; however, there is still a lack of consensus on the best diagnostic and therapeutic approach for these patients [2].

Here, we report on a case of TOF accompanied by an absent left pulmonary artery and further complicated by major aortopulmonary collateral arteries (MAPCA).

References

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Dr. Dilek Erer

Department of Cardiovascular Surgery
Gazi University Medical School

Gazi Üniversitesi Tip Fakültesi Kalp Damar Cerrahisi

AD Besevler

06690 Ankara

Turkey

Phone: + 90 50 53 19 31 90

Fax: + 90 31 22 12 90 14

Email: dilekerer@hotmail.com

Email: dilekerer@yahoo.com