Download PDF
Semin Thromb Hemost 1997; 23(4): 357-363
DOI: 10.1055/s-2007-996109
Copyright © 1997 by Thieme Medical Publishers, Inc.

Erythromelalgia: A Pathognomonic Microvascular Thrombotic Complication in Essential Thrombocythemia and Polycythemia Vera

Perry J.J. van Genderen, Jan J. Michiels
  • From the Department of Internal Medicine II and Hematology, Erasmus University Hospital Dijkzigt and Goodheart Institute, Rotterdam, The Netherlands.
Further Information

Publication History

Publication Date:
08 February 2008 (online)

  PDF Download  Permissions and Reprints

Abstract

Erythromelalgia is a characteristic thrombotic complication in patients with the myeloproliferative disorders, essential thrombocythemia and polycythemia vera. In this minireview, which is based on more than 20 years of clinical observations and intervention studies, the clinical manifestations, treatment, and pathogenesis of erythromelalgia are discussed.

Keywords:

Erythromelalgia - essential thrombocythemia - polycythemia vera - myeloproliferative disorders - thrombosis