Intestinal Neuronal Dysplasia of the Myenteric Plexus - A New Entity in Humans?

Abstract

Intestinal neuronal dysplasia is a rare cause of bowel obstruction in neonates and infants, the diagnosis of which poses a formidable challenge to both clinicians and pathologists alike. The importance of this entity lies not only in the fact that it mimics Hirschsprung's disease, but also in that untreated cases may prove fatal. The authors describe one such case of enigmatic entity of intestinal neuronal dysplasia of the myenteric plexus.

Key words

Hirschsprung's disease - intestinal neuronal dysplasia

References

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