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Neuropediatrics 1984; 15(2): 95-98
DOI: 10.1055/s-2008-1052348
© Georg Thieme Verlag KG Stuttgart · New York

Sturge-Weber Disease - Neurophysiological Evaluation of a Case with Secondary Epileptogenesis, Successfully Treated with Lobe-Ectomy

I.  Rosén1 , L.  Salford2 , Lena  Starck3
  • 1Department of Clinical Neurophysiology, University Hospital, S-22185 Lund, Sweden
  • 2Department of Neurosurgery, University Hospital, S-22185 Lund, Sweden
  • 3Department of Pediatrics, University Hospital, S-22185 Lund, Sweden
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Publication History

Publication Date:
19 March 2008 (online)

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Abstract

A case of Sturge-Weber's disease with a generalized seizure at 7 months of age is described, followed 7 months later by the development of very frequent and therapy resistent myoclonic astatic fits. The neurophysiological evaluation indicated a primary lesion in the right occipital area followed by signs of secondary epileptogenesis. The patient was cured by a right-sided occipital lobe-ectomy including an area of leptomeningeal angiomatosis.

Key words

Sturge-Weber disease - Epilepsy - EEG - Visual evoked response - Neurosurgical treatment