Download PDF
Neuropediatrics 1990; 21(4): 213-214
DOI: 10.1055/s-2008-1071499
Case report

© Georg Thieme Verlag KG Stuttgart · New York

Benign Paroxysmal Tonic Upgaze of Childhood - A New Syndrome*

Th.  Deonna , E.  Roulet , H. U. Meyer
  • Pediatric Department (Neuropediatric Unit), CHUV, Lausanne, Switzerland
* Paper presented at the IVth Congress of the „Société Européenne de Neurologie Pédiatrique”, Barcelona, 23-24. 11. 1989
Further Information

Publication History

Publication Date:
19 March 2008 (online)

Also available at
  PDF Download  Permissions and Reprints

Abstract

A child with intermittent upward deviation of the eyes starting at 9 months of age, compensating bending forward of the head, nystagmus on attempted downward gaze and a mild gait ataxia is described.

The symptoms gradually disappeared between 3 and 4 years of age.

Four cases with identical clinical findings have been initially described by Ouvrier in Australia (5) as "benign paroxysmal tonic upgaze of childhood". It is apparently a new syndrome.

Key words

Paroxysmal disorder - Eye movement disorders - Tonic eye deviation - Infantile nystagmus - Childhood ataxia - Infancy