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DOI: 10.3233/JPN-2010-0449
Subacute sclerosing panencephalitis with an atypical presentation: A case report
Subject Editor:
Publication History
10 September 2009
21 February 2010
Publication Date:
30 July 2015 (online)
Abstract
Subacute sclerosing panencephalitis is almost always fatal with a varying clinical course of illness. It is characterized by slow progression and rarely manifests with a fulminant and rapid course. Atypical presentations such as generalized seizures, visual loss, hemiparesis, non-convulsive status epilepticus and isolated extrapyramidal symptoms can be observed rarely. We report an 11-year-old boy presenting with atypical symptoms initially such as complex partial seizures, chorea and electrographic status epilepticus. The patient was lost within 5 months, which is suitable for a fulminant course. Children presenting with atypical acute or subacute neurologic symptoms should be examined for subacute sclerosing panencephalitis, especially if they have no risk factors for hereditary neurodegenerative and/or neurometabolic diseases.