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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2015; 25(03): 280-283
DOI: 10.4103/0971-3026.161456
Musculoskeletal Radiology

Polyostotic fibrous dysplasia associated with intramuscular myxomas: Mazabraud syndrome

Jose Daniel Samper Wamba
Department of Radiology, University Hospital of León, León, Spain
,
Maria Jose Fernandez Bermudez
Department of Radiology, University Hospital of León, León, Spain
,
Teresa Lorenzo Dominguez
Department of Radiology, University Hospital of León, León, Spain
,
Luis Ramos Pascua
Department of Orthopaedics and Traumatology, University Hospital of León, León, Spain
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

The authors report a new case of Mazabraud syndrome in a 69-year-old woman complaining of pain in her right thigh. Plain radiographs demonstrated radiological findings consistent with polyostotic fibrous dysplasia of the right femur and tibia. Magnetic resonance imaging (MRI) study showed soft tissue tumors located in the vastus intermedius muscle with typical signal features of intramuscular myxomas. Biopsy was not performed because of its benign nature. Symptomatic treatment was prescribed and all the lesions remained 1 year after the diagnosis.

Keywords

Fibrous dysplasia - intramuscular myxomas - Mazabraud syndrome


Publication History

Article published online:
30 July 2021

© 2015. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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