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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2008; 18(04): 352-354
DOI: 10.4103/0971-3026.43841
Obstetric USG Symposium

Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks

Alpa H Bharati
Department of Radiology, Lokmanya Tilak Municipal General Hospital, Sion, Mumbai, India
,
Ajita Naware
Department of Radiology, Lokmanya Tilak Municipal General Hospital, Sion, Mumbai, India
,
Suleman A Merchant
Department of Radiology, Lokmanya Tilak Municipal General Hospital, Sion, Mumbai, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Absent pulmonary valve syndrome is a rare congenital anomaly, usually seen in association with a ventricular septal defect. It has been reported to occur in 3-6% of cases of tetralogy of Fallot. Absence of the pulmonary valve results in a dilated main pulmonary artery, which can be seen as a cystic, pulsatile, paracardiac lesion on antenatal USG. Such a lesion, though rare, can easily be detected. We report a case of this rare anomaly which was present in association with a ventricular septal defect, tetralogy of Fallot, and dextrocardia. The case was detected at 26 weeks of gestation.

Keywords

Pulmonary valve - antenatal US - dextrocardia - tetralogy of Fallot


Publication History

Article published online:
31 July 2021

© 2008. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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