Congenital nasal pyriform aperture stenosis: A rare cause of nasal airway obstruction in a neonate

Abstract

Congenital nasal pyriform aperture stenosis (CNPAS) is a rare cause of nasal airway obstruction that clinically mimics choanal atresia, but needs to be differentiated from the latter because of the widely divergent modes of management. We present a case of CNPAS, to highlight the importance of recognizing the classic signs of CNPAS on cross-sectional imaging.

Keywords

Choanal atresia - CNPAS - holoprosencephaly - megaincisor - pyriform aperture stenosis

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