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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2012; 22(01): 54-57
DOI: 10.4103/0971-3026.95405
GI Radiology

CT scan diagnosis of hepatic adenoma in a case of von Gierke disease

Bipin Valchandji Daga
Department of Radiodiagnosis and Imaging Sciences, Dr. Vaishampaiyan Memorial Government Medical College (VM GMC), Solapur, Maharashtra, India
,
Vaibhav R Shah
Department of Radiodiagnosis and Imaging Sciences, Dr. Vaishampaiyan Memorial Government Medical College (VM GMC), Solapur, Maharashtra, India
,
Rahul B More
Department of Radiodiagnosis and Imaging Sciences, Dr. Vaishampaiyan Memorial Government Medical College (VM GMC), Solapur, Maharashtra, India
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Abstract

Hepatic adenoma is a well-defined, benign, solitary tumor of the liver. In individuals with glycogen storage disease I, adenoma tends to occur at a relatively younger age and can be multiple (adenomatosis). Imaging plays a pivotal role in diagnosing hepatic adenoma and in differentiating adenoma from other focal hepatic lesions. Especially in patients with von Gierke disease, in addition to the associated hepatomegaly caused by steatohepatitis and the diffusely reduced attenuation of the liver parenchyma seen on CT, there may be more than one hepatic adenoma in up to 40% of patients. Malignant degeneration of hepatic adenoma into hepatocellular carcinoma can occur and hence imaging is important for prompt diagnosis of adenoma and its complications. In this case report, we present a case of liver adenoma diagnosed by CT scan in a patient with von Gierke disease.

Keywords

CT - Hepatic adenoma - von Gierke disease


Publication History

Article published online:
30 July 2021

© 2012. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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