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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2014; 35(03): 231-233
DOI: 10.4103/0971-5851.142042
CASE REPORT

Immature teratoma at umbilicus region presenting as exomphalos: A case report with review of literature

Lakshmi V. Chavali
Department of Pathology, Rangaraya Medical College, Kakinada, East Godavari, Andhra Medical College, Andhra Pradesh, India
,
R Bhaskar
Department of Pathology, Andhra Medical College, Visakhapatnam, Andhra Pradesh, India
,
J Bhaskar Reddy
Department of Pediatric Surgery, Rangaraya Medical College, Kakinada, East Godavari, Andhra Medical College, Andhra Pradesh, India
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Abstract

Umbilical cord neoplasms are rare. Teratomas, which are accepted as the only true neoplasms at this site, are exceptional. These tumors are polymorphic in their presentation and are often associated with other abnormalities, with exomphalos being the most common abnormality. Histologically these tumors show mature tissues from all the three-germ layers. Immature elements as seen in our case are rare. Germ cells which have gone astray during embryonic development are thought to be the cells of origin of these tumors.

Keywords

Exomphalos - teratoma - umbilical cord


Publication History

Article published online:
19 July 2021

© 2014. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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