Multilocular Cystic Renal Cell Carcinoma: A Rare Entity with Review of Literature

Shailja Puri Wahal; Kavita Mardi

doi:10.4103/0974-2727.129093

Journal of Laboratory Physicians, Table of Contents

CC BY-NC-ND 4.0 · J Lab Physicians 2014; 6(01): 050-052
DOI: 10.4103/0974-2727.129093

Case Report

Multilocular Cystic Renal Cell Carcinoma: A Rare Entity with Review of Literature

Shailja Puri Wahal

Department of Pathology, Indira Gandhi Medical College, Shimla, Himachal Pradesh, India

,

Kavita Mardi

Department of Pathology, Indira Gandhi Medical College, Shimla, Himachal Pradesh, India

› Author Affiliations

Abstract

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ABSTRACT

Multilocular cystic renal cell carcinoma (MCRCC) represents a rare variant of clear cell renal cell carcinoma (RCC). MCRCC has been recognized as a separate subtype of RCC in the 2004 World Health Organization (WHO) classification of adult renal tumors. MCRCC is diagnosed on the basis of strict histological criteria according to 2004 WHO classification. The chief differentials diagnosis to be considered include cystic nephroma, cystic clear cell carcinoma, clear cell papillary renal cell carcinoma and tubulocystic carcinoma. Only few cases of MCRCC are reported in literature. This case is being highlighted for its rarity and so as to avoid a misdiagnosis as conventional RCC.

Key words:

Multilocular cystic renal cell carcinoma - clear cell RCC - kidney

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References

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