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CC BY-NC-ND 4.0 · J Lab Physicians 2011; 3(01): 056-058
DOI: 10.4103/0974-2727.78571
Case Report

Epignathus with Fetiform Features

Kumar Sunil Y.
Department of Pathology , KS Hegde Medical Academy, Deralakatte, Mangalore, India
,
Shrikrishna U.
Department of Radiology, KS Hegde Medical Academy, Deralakatte, Mangalore, India
,
Jayaprakash Shetty
Department of Pathology , KS Hegde Medical Academy, Deralakatte, Mangalore, India
,
Aishwarya Sitaram
Department of Pathology , KS Hegde Medical Academy, Deralakatte, Mangalore, India
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ABSTRACT

Epignathus is an extremely rare oropharyngeal teratoma that commonly arises from the palate, leading to a high mortality (80-100%) due to airway obstruction in the neonatal period. We present a case of epignathus immature teratoma with fetiform features, originating from basisphenoid in a 28-week preterm male baby, who succumbed to death immediately after birth. Since epignathus is a life-threatening condition at the time of delivery, a prenatal diagnosis is essential to coordinate the treatment and appropriate management by securing the airway, either by endotracheal intubation or tracheostomy followed by complete resection of the tumor.

Keywords

Epignathus - fetiform - immature teratoma - resection


Publication History

Article published online:
29 January 2020

© 2011.

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