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CC BY-NC-ND 4.0 · J Lab Physicians 2012; 4(01): 053-055
DOI: 10.4103/0974-2727.98677
Case Report

Cutaneous Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge

Akshay Bali
Department of Pathology, Jawaharlal Nehru Medical College, Belgaum, India
,
Maitrayee Roy
Department of Pathology, Jawaharlal Nehru Medical College, Belgaum, India
,
Panduranga Chikkannaiah
Department of Pathology, Jawaharlal Nehru Medical College, Belgaum, India
,
Vijayalaxmi Dhorigol
Department of Pathology, Jawaharlal Nehru Medical College, Belgaum, India
› Author Affiliations Source of Support: Nil
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ABSTRACT

Clear cell sarcoma is a deep-seated, exceedingly rare aggressive tumor, typically involving the tendons and aponeuroses with melanocytic differentiation and a distinct genetic background. A primary dermal location is rarer. It exhibits histological, immunohistochemical, and ultrastructural similarities with the more common primary (or metastatic) malignant melanoma causing major diagnostic confusion. We describe a case of primary cutaneous clear cell sarcoma arising in the right lower extremity of a 40-year-old male patient.

Keywords

Clear cell sarcoma - cutaneous - malignant melanoma


Publication History

Article published online:
09 May 2020

© 2012.

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